Vesical Hemangioma in a Patient with Klippel-Trenaunay-Weber Syndrome

A 3-year-old child with Klippel-Trepanauy-Weber syndrome (KTWS), was admitted to our hospital with recurrent episodes of hematuria. Subsequent clinical history revealed 2 episodes of hematuria some weeks before, not initially mentioned by the parents. Urine analyses were negative for erythrocytes and proteinuria. The child manifested a normocytic anemia (hemoglobin, 9.9 g/dL; mean corpuscular volume, 74 μm3; iron, 13 μg/d). Coagulation tests were normal; her d-dimers were 2060. An ultrasound examination of the urinary tract demonstrated a giant mass in the vesical dome (Figure 1).

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